Heteromorphism 18ph+ : with or without reproductive consequences?

Ann Genet. 2001 Jul-Sep;44(3):139-42. doi: 10.1016/s0003-3995(01)01079-6.

Abstract

Heteromorphism or chromosomal variants are usually attributed to structural variations in constitutive heterochromatin. In the case of chromosome 18, 25 cases of 18ph+ have been reported to date. Using the Primed In Situ Labelling technique (PRINS) to study 2 new cases of 18ph+, we have been able to confirm their molecular nature and assuming a mechanism of formation. Although such chromosomal variants are usually thought to have no adverse clinical consequence, a review of the literature shows that many cases were diagnosed because of recurrent abortion, malformed or mentally retarded children suggesting the possible relationship between 18ph+ and such clinical outcomes.

Publication types

  • Case Reports

MeSH terms

  • Amniotic Fluid / metabolism
  • Chromosome Aberrations*
  • Chromosome Banding
  • Chromosomes, Human, Pair 18*
  • Female
  • Humans
  • Hydrocephalus / genetics
  • Intellectual Disability / genetics
  • Karyotyping
  • Lymphangioma, Cystic / genetics
  • Pregnancy
  • Prenatal Diagnosis