Epidemiology of progressive supranuclear palsy. ESGAP Consortium. European Study Group on Atypical Parkinsonisms

Neurol Sci. 2001 Feb;22(1):101-3. doi: 10.1007/s100720170065.

Abstract

Progressive supranuclear palsy (PSP) is a rare form of parkinsonism. The incidence rates are about 0.3-1.1 cases per 100,000 persons. The only two case-control studies performed up to now show conflictual results as regards education and residence in rural areas. Recently, a cluster of PSP and atypical parkinsonism has been observed in French Antilles. The hypothesis is that a consumption of both tropical fruit and herbal tea may be associated with PSP onset. Some PSP families with a probably autosomal dominant transmission have been described. A high frequency of a tau haplotype (H1/H1) associated with PSP is reported by some authors. The significance of this association is still not clear. We have performed a case-control study on 58 PSP cases, 116 hospital controls and 58 population controls.

Publication types

  • Multicenter Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Age of Onset
  • Beverages / adverse effects
  • Environmental Exposure
  • Female
  • Genetic Testing
  • Guadeloupe / epidemiology
  • Humans
  • Incidence
  • Male
  • Mutation / genetics
  • Occupational Diseases / epidemiology
  • Prevalence
  • Risk Factors
  • Sex Factors
  • Supranuclear Palsy, Progressive / epidemiology*
  • Supranuclear Palsy, Progressive / physiopathology
  • tau Proteins / genetics

Substances

  • tau Proteins