[Pulmonary hyalinising granuloma: report of 2 original cases with cervicofacial and orbital involvement]

Rev Med Interne. 2001 Mar;22(3):284-91. doi: 10.1016/s0248-8663(00)00330-1.
[Article in French]

Abstract

Introduction: Pulmonary hyalinizing granuloma is a rare fibrosing nodular disease of the lung characterized by its histological appearance, which includes at the center of the lesion a dense network of concentric hyalinized collagen lamella surrounded by perivascular lymphoplasmacytic infiltrate that rarefies in the center of the nodule.

Exegesis: We report two new cases: the first with laryngeal (endoluminal tumor-like), orbital (subeyelid nodule) and mesenteric (9 x 6 cm mass) location of hyalinizing granuloma; the second with cervical, facial (trismus), orbital (pseudotumor) and limb (ankylosing elbow) fibrosis.

Conclusion: The extrapulmonary diffusion of the disease is extremely rare. In one of the cases, with corticosteroids and after a follow-up of 12 months, the pulmonary tumors vanished but the fibrosis resolved only partially.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adult
  • Face
  • Female
  • Granuloma / complications*
  • Humans
  • Hyalin*
  • Laryngeal Diseases / etiology*
  • Lung Diseases / complications*
  • Mesentery
  • Orbital Diseases / etiology*