En bloc heterotopic auxiliary liver and bilateral renal transplant in a patient with homozygous protein C deficiency

M Angelis; C H Pegelow; F A Khan; R Verzaro; A G Tzakis

doi:10.1067/mpd.2001.109199

En bloc heterotopic auxiliary liver and bilateral renal transplant in a patient with homozygous protein C deficiency

J Pediatr. 2001 Jan;138(1):120-2. doi: 10.1067/mpd.2001.109199.

Authors

M Angelis¹, C H Pegelow, F A Khan, R Verzaro, A G Tzakis

Affiliation

¹ Department of Surgery, Division of Liver Transplant, University of Miami School of Medicine, Miami, Florida, USA.

PMID: 11148525
DOI: 10.1067/mpd.2001.109199

Abstract

An 8-year-old girl with homozygous protein C deficiency who had undergone maintenance dialysis since birth because of renal veins with thrombosis was treated with an en bloc heterotopic auxiliary liver and bilateral renal transplantation. The reconstitution of protein C activity by auxiliary liver transplantation facilitated successful renal transplantation.

Publication types

Case Reports

MeSH terms

Child
Choledochostomy
Female
Homozygote
Humans
Kidney Failure, Chronic / etiology*
Kidney Failure, Chronic / surgery*
Kidney Transplantation / methods*
Liver Transplantation / methods*
Phenotype
Protein C Deficiency / complications*
Protein C Deficiency / genetics
Protein C Deficiency / surgery*
Renal Dialysis
Renal Veins
Transplantation, Heterotopic / methods*
Venous Thrombosis / etiology