Outcome in infants with pulmonary atresia, intact ventricular septum, and right ventricle-dependent coronary circulation

Am J Cardiol. 2000 Dec 1;86(11):1272-4, A9. doi: 10.1016/s0002-9149(00)01220-0.

Abstract

Management of all patients with pulmonary atresia, intact ventricular septum, and right ventricle-dependent coronary circulation (n = 12) with staged surgery directed toward a Fontan palliation resulted in an 83% 5-year actuarial survival. Both deaths in the study were presumably related to coronary ischemia and occurred in the first 4 months of life.

Publication types

  • Comparative Study
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Abnormalities, Multiple* / diagnosis
  • Abnormalities, Multiple* / surgery
  • Angiography
  • Cardiac Catheterization
  • Cardiac Surgical Procedures / methods
  • Child
  • Child, Preschool
  • Coronary Vessel Anomalies / diagnosis
  • Coronary Vessel Anomalies / surgery*
  • Echocardiography
  • Heart Septal Defects, Ventricular / diagnosis
  • Heart Septal Defects, Ventricular / surgery*
  • Heart Ventricles / abnormalities*
  • Heart Ventricles / diagnostic imaging
  • Humans
  • Infant
  • Infant, Newborn
  • Pulmonary Atresia / diagnosis
  • Pulmonary Atresia / surgery*
  • Retrospective Studies
  • Treatment Outcome
  • Vascular Fistula / diagnosis
  • Vascular Fistula / surgery*